Successful outcome of pregnancy in Bernard -Soulier Syndrome with temporary endovascular balloon occlusion of uterine arteries: A Case Report

Abstract

Bernard-Soulier Syndrome (BSS) is a rare congenital bleeding disorder, mainly inherited in an autosomal recessive pattern.The phenotype of BSS varies widely depending on particular mutation.Pregnancy in BSS is associated with a high risk of bleeding for mother and neonate, and there is no consensus about ideal management of these patients.

AIM

Use of perioperative endovascular balloon occlusion of internal iliac arteries (uterine artery), a minimally invasive technique that reduces blood loss and transfusion requirement in high bleedingrisk patients like BSS.

Case Presentation

It describes a successful pregnancy outcome with endovascular intervention in a woman with BSS who was closely monitored in pregnancy,peripartum, postpartum period,and had a planned birth.

Conclusion

 Minimally invasive and effective endovascular prophylactic measures against bleeding reduces blood loss, transfusion requirement, platelet refractoriness and hospital stay during caesarean section in BSS